Male breast cancer is a very rare disease with an incidence of about 0.5–1% comparing with the one offemale breast cancer but relatively little is known about its cause. Treatment strategies for breast cancer in malesare derived from studies performed among females. The probable reasons behind the frequent, late diagnosespresented at stages III or IV might be the lack of awareness. The rarity of the disease precludes large prospectiverandomized clinical trials. This study reviews male breast cancer and its risk factors, recommendations fordiagnosis and the management of patients with male breast cancer.